Hypoxia due to intrapulmonary vascular dilatation in a toddler with a congenital portacaval shunt: Case report

Mohammed T. Alsamri, Mohamed A. Hamdan, Mohamed Sulaiman, Hassib Narchi, Abdul Kader Souid

Research output: Contribution to journalArticlepeer-review

Abstract

Background: The term hepatopulmonary syndrome typically applies to cyanosis that results from "intrapulmonary vascular dilatation" due to advanced liver disease. Similar findings may result from a congenital portosystemic shunt without liver disease. An adverse consequence of such shunts is intrapulmonary vascular dilatation, which affects the microvascular gas exchange units for oxygen. Case presentation: Here, we describe a toddler with chronic cyanosis, exercise intolerance, and finger clubbing due to a malformation shunt between the portal vein and the inferior vena cava. A transcatheter embolization of the shunt resulted in resolution of his findings. Conclusions: Congenital portosystemic shunts need to be considered in the differential diagnosis of cyanosis.

Original languageEnglish
Article number49
JournalBMC Pulmonary Medicine
Volume19
Issue number1
DOIs
Publication statusPublished - Feb 22 2019

Keywords

  • Cyanosis
  • Finger clubbing
  • Hepatopulmonary syndrome
  • Hypoxia
  • Portosystemic shunt
  • Venous malformation

ASJC Scopus subject areas

  • Pulmonary and Respiratory Medicine

Fingerprint

Dive into the research topics of 'Hypoxia due to intrapulmonary vascular dilatation in a toddler with a congenital portacaval shunt: Case report'. Together they form a unique fingerprint.

Cite this